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Pathways of ammonia detoxification to GLN in muscles linked to Increased usage of your BCAA and α-KG (cataplerosis) and recommended results of BCAA and phenylbutyrate in subjects with liver cirrhosis or UCD. Constructive influence of BCAA on ammonia detoxification to GLN may be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phen